Ewing Sarcoma of Orbit with Intracranial Extension

Abstract

Ewing sarcoma causing unilateral proptosis in a child is unusual presentation. A
young girl presented with painless proptosis of left eye with restricted eye
movements. Her radiology revealed a large soft tissue mass causing destruction
of lateral orbital wall and zygomatic arch measuring 2.0 × 3.0 cm. Total excision
of intracranial and intra orbital part of the tumor brought about substantial relief.
The clinical and radiological presentation and management of this entity are
discussed.
Key words: Sphenoid bone, Ewing sarcoma, orbital proptosis, primitive
neuroepithelial tumor (PNET), radiology, small round cell tumor, surgery.