Unilateral Exotropic Type II Duane’s Retraction Syndrome Associated with Tetralogy of Fallot: A Case Report

Doi: 10.36351/pjo.v39i4.1696

Abstract

Duane’s retraction syndrome is a rare congenital cranial disorder and special form of strabismus that manifests with the limitation of ocular movements in horizontal gaze, globe retraction, and narrowing of the palpebral fissure in adduction. Its causeis a teratogenic cranial innervational defect at the 4th-8th weeks of gestation. It is estimated that up to one third of these patients may have other congenital non-ocular anomalies. In this case, we present an association of unilateral exotropictype II Duane’s retraction syndrome and tetralogy of Fallot in an eleven years old boy. He had no other systemic disease or congenital anomaly, and his family history was negative for strabismus and congenital heart disease. Duane’s retraction syndrome can be associated with tetralogy of Fallot due to the matching time of gestational development of these two conditions, although this may be coincidental.