Posterior Uveal Effusion Syndrome Following Ectopia Lentis Surgery in a Case with Marfan's Syndrome

Abstract

To describe a case of acute uveal effusion with hypermetropic refraction that was limited to the posterior pole in a patient with Marfan’s syndrome and bilateral ectopia lentis

who underwent surgery for her left eye. A 22-year-old female with Marfan’s syndrome and concomitant bilateral ectopia lentis was admitted for surgery on her left eye. On post- operation day one, we detected a shallow posterior uveal effusion (UE) and disc edema that did not include peripheral retina. Shallow posterior UE and disc edema were almost totally recovered after 3 weeks of the operation. To the best of our knowledge, this is the first case of Marfan’s syndrome with concomitant ectopia lentis in medical literatures who had uveal effusion limited to the posterior pole after surgery. It is considered as Marfan's syndrome might be a predisposing factor for posterior UE.

Key words: Choroidal diseases, Lentis Ectopia, Hypermetropia, Marfan's syndrome, posterior uveal effusion syndrome.